Evans Syndrome

  • Autoimmune hemolytic anemia (AIHA)
  • Immune thrombocytopenia
  • and or autoimmune neurtopenia
  • substantial portion has Autoimmune lymphoproliferative syndrome (ALPS)

Treatment

  • IVIG is used commonly to treat AIHA
  • Steroid: initially effective, most relapse after stopping therapy, alternative therapy is required